Pathways of ammonia detoxification to GLN in muscles associated with enhanced use from the BCAA and ?-KG (cataplerosis) and prompt results of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Good impact of BCAA on ammonia detoxification to GLN can be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbutyrate decr